Quick Answer: How Long Do Babies With HLHS Live?

How long does Fontan procedure last?

The procedure will last about five hours.

Recovery from Fontan surgery usually requires a two- or three-week hospital stay that will start in the cardiac intensive care unit (CICU).

Learn more about postoperative care following surgeries for hypoplastic left heart syndrome..

How old is the oldest person with HLHS?

The oldest living person with HLHS is their 30s. Ultimately, the Cribbs hope and pray that Leigh Ann has a long life ahead of her. Texas Children’s Hospital – part of the Children’s Miracle Network Hospitals is excited to celebrate the third annual Children’s Hospital Week from March 18-24.

Can Hlhs be cured?

Hypoplastic left heart syndrome is treated through several surgical procedures or a heart transplant. Your child’s doctor will discuss treatment options with you. If the diagnosis has been made before the baby is born, doctors usually recommend delivery at a hospital with a cardiac surgery center.

Does Hlhs run in families?

Doctors don’t know why HLHS happens, but it does run in families. Some experts think that what the mother eats, drinks, or comes into contact with during pregnancy may also increase the risk that their baby will have HLHS.

What causes HLHS babies?

HLHS is the result of under-development of sections of the fetal heart during the first eight weeks of pregnancy. But it’s not understood why some babies’ hearts don’t develop normally. Congenital heart defects usually occur sporadically with no clear reason for their development.

Can you live with only half a heart?

The syndrome is a rare inherited disorder in which the left half of the heart is undersized and cannot perform its function of pumping blood to the body. … Without surgery, it is fatal.

How many babies are born with HLHS each year?

The Centers for Disease Control and Prevention (CDC) estimates that each year about 1,025 babies in the United States are born with hypoplastic left heart syndrome. 1 In other words, about 1 out of every 3,841 babies born in the United States each year is born with hypoplastic left heart syndrome.

What is the survival rate of hypoplastic right heart syndrome?

They found that first-year survival was low for HLHS (22.6%) and for pulmonary atresia with intact ventricular septum (PA- IVS; 50%), a form of hypoplastic right ventricle.

How long do HLHS patients live?

Most infants die within the first two weeks of life, with an average age at death of 4.5 days (31,33,34). Some patients with HLHS, however, can survive beyond sixty days, without any surgical intervention through the development of pulmonary hypertension (8,33).

Is Hlhs a disability?

If your child has been born with Hypoplastic Left Heart Syndrome it may help to know that he or she will automatically qualify for Social Security Disability benefits because the SSA has recently determined the condition meets the criteria for Compassionate Allowance status.

How rare is Hlhs?

Hypoplastic left heart syndrome is a rare disorder that affects males (67 percent) more often than females. The estimated prevalence of the disorder is 1 in 100,000 live births. Hypoplastic left heart syndrome accounts for 7-9 percent of all congenital heart defects.

What are the chances of having another baby with a heart defect?

Congenital heart defects (CHD) are common and impact more than 40,000 babies each year. The chance of having another baby with a heart defect depends on your child’s specific diagnosis, but in general, the risk is estimated to be between 2-3 percent.

What are my chances of having another baby with hypoplastic left heart syndrome?

These do require intervention but often a two-ventricle (pumping chamber) circulation is possible. When there is recurrence of congenital heart disease in a family previously affected with Hypoplastic Left Heart Syndrome, about one third of the new babies will have Hypoplastic Left Heart Syndrome like their sibling.

Can Hlhs be detected before birth?

Prenatal ultrasound can identify a problem with the baby’s heart. The diagnosis of HLHS is made by fetal echocardiogram as early as 16 weeks gestation.

Is Hlhs genetic?

HLHS typically occurs sporadically (randomly), in otherwise normal babies with no family history of HLHS. In a few children, isolated HLHS is known to be genetic. These cases may be due to mutations in the GJA1 gene with autosomal recessive inheritance, or the NKX2-5 gene with autosomal dominant inheritance.

Can a baby survive with half a heart?

A baby with only half a heart has finally been allowed home after he survived risky open-heart surgery at just four days old. Reggie Aslin was born with hypoplastic left heart syndrome (HLHS), a rare defect which means half of his heart did not form properly.

How long does the Glenn procedure take?

The Glenn procedure requires open heart surgery and will take about three hours to complete. During that time your baby will be on a heart-lung machine to temporarily take over breathing and blood circulation.